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Bickerstaff’s encephalitis

Evidence: Antibody

Names

Bickerstaff encephalitis
Bickerstaff's brainstem Encephalitis

Description

Bickerstaff's brainstem encephalitis (BBE) is an immune disorder of unknown cause. It involves specific anti-bodies that attack parts of the brain. It is characterized by acute, progressive brain dysfunction. Associated with Cerebellar Ataxia. 

Bloggers

N/A

Prevalence

The precise incidence and prevalence of BBE is currently unknown. A nationwide survey of patients in Japan with BBE estimated that the annual incidence of BBE affects approximately 100 individuals [Koga 2013]

Notes:
1. Overlap with other antibody syndromes makes it hard to diagnose and distinguish.
2. Bickerstaff Encephalitis is very rare.

Typical Age of onset

Mostly reported in adults (age range N/A)

Symptoms

  • Double vision

  • Ataxia (paralysis)

  • Disturbance of consciousness

  • Headache

  • Facial palsy

  • Pupil abnormalities

  • Involuntary eye movements

  • Disturbance of consciousness

  • Overactive reflexes

Source: Mayo Clinic, Healthline